Publication: Polyarteritis nodosa in case of familial Mediterranean fever
Loading...
Date
2018
Authors
Journal Title
Journal ISSN
Volume Title
Publisher
TURKISH J PEDIATRICS
Abstract
Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by recurrent self-limited attacks of fever accompanied by peritonitis, pleuritis, and arthritis. Protracted febrile myalgia syndrome (PFMS) is a rare form of vasculitic disease which is an uncommon dramatic manifestation of FMF, characterized by severe crippling myalgia and high fever. Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis affecting medium or small arteries. It is rarely observed in children, but its incidence increases in the presence of FMF. In this article we described a 14-yea-old child diagnosed with FMF associated with PAN. Physicians should be aware of this possible association.
Description
Keywords
familial Mediterranean fever, protracted febrile myalgia syndrome, polyarteritis nodosa, PROTRACTED FEBRILE MYALGIA, GENE-MUTATIONS, CHILDREN, FMF, CRITERIA, PATIENT