Cleidocranial dysostosis: report of a case

Abstract

This case of cleidocranial dysostosis showed nearly 40 accessory teeth and the unerupted teeth on radiological examinations. Other diagnostic procedures found hypoplasia in maxillary and zygomatic bones, deep palate, open fontanel and open sutures, the collapse of sagittal suture, and aplasia of the clavicle. There were some abnormalities of the fingers. Under general anesthesia eleven supernumerary teeth in the mandible and eight in the maxilla were surgically extracted. Upper and lower removable acrylic appliances were fabricated.